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Transfusion Medicine and Hemotherapy
Article . 2006 . Peer-reviewed
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Transfusion Medicine and Hemotherapy
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Transfusion Medicine and Hemotherapy
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Transfusion Medicine and Hemotherapy
Article . 2006
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Autoimmune Lymphoproliferative Syndrome – Impaired Regulation of the Immune Response by Impaired Induction of Apoptosis

descriptionPublicationkeyboard_double_arrow_right Article 01 Jan 2006 English Publisher:S. Karger AGJournal:Transfusion Medicine and Hemotherapy, volume 33, pages 71-79 (issn: 1660-3796, eissn: 1660-3818, Copyright policy )
Authors: Robert Brawura-Biskupski-Samaha; Tomasz Grzela;

doi: 10.1159/000090202

Autoimmune Lymphoproliferative Syndrome – Impaired Regulation of the Immune Response by Impaired Induction of Apoptosis

Abstract

Autoimmune lymphoproliferative syndrome (ALPS) is an inherited disease hindering apoptosis of lymphocytes. It includes mutations in genes coding for various components of the apoptotic pathway: CD95 (ALPS 0 and ALPS Ia), CD178 (ALPS Ib) and caspase-10 (ALPS II). Moreover, patients with genetically inherited caspase-8 or other components of apoptosis-inducing pathway deficiencies (ALPS III) have been described recently. In addition, ALPS-like clinical patterns, including Dianzani’s autoimmune lymphoproliferative disease (DALD), were characterized. In this review, we summarize currently known types of ALPS and characterize their immunological and molecular background.

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selected citations
These citations are derived from selected sources.
This is an alternative to the "Influence" indicator, which also reflects the overall/total impact of an article in the research community at large, based on the underlying citation network (diachronically).
BIP!Citations provided by BIP!
popularity
This indicator reflects the "current" impact/attention (the "hype") of an article in the research community at large, based on the underlying citation network.
BIP!Popularity provided by BIP!
influence
This indicator reflects the overall/total impact of an article in the research community at large, based on the underlying citation network (diachronically).
BIP!Influence provided by BIP!
impulse
This indicator reflects the initial momentum of an article directly after its publication, based on the underlying citation network.
BIP!Impulse provided by BIP!
5
Average
Average
Top 10%
gold
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