Otosclerosis is a disease characterized by abnormal bony growth and remodeling around the otic capsule. Although adults make up the majority of patients, otosclerosis is also encountered in children. However, the literature on juvenile otosclerosis is still limited. The main therapeutic options for children with otosclerosis are hearing aids or stapes surgery. Despite many years of treating pediatric patients with stapes surgery, the issue of whether to perform the operation is still a subject of debate. To identify suitable literature on juvenile otosclerosis, a search was performed using the following databases: PubMed, Web of Science, and Medline, and based on the search criteria 19 articles were found suitable for the review. The current evidence indicates that stapes surgery for juvenile otosclerosis is a safe and effective procedure which leads to closure of the air-bone gap over both short and long terms. Complications of stapes surgery are extremely rare and in the majority of cases comprise transient vertigo. Age itself should not be a contraindication to stapes surgery for juvenile otosclerosis.