Congenital posterior urethral-perinal fistula is a rare anomaly of which there have been reported only one case to date. This report outline the simple clinical presentation, diagnosis and simple technique surgical management. Congenital posterior urethral-perineal fistula is a rare anomaly. This is a rare case in the world literature. There are reported only six cases since 1964. Dr. William C. Brown, Dillon, Heusele has reported one case (diagnosis and new surgical technique). Other authors have reported rare cases: Le Duc has reported one instance ofan urethral-rectal fistula in the absence of any anorectal abnormality. Out of the 7 cases previously reported one is actually an urethral scrotal fistula but it is included since it has a similar embrylogic origin to the rest of the series.