Primary cutaneous anaplastic large T-cell lymphoma CD30+ is a rare cutaneous lymphoma, which belongs to the group of cutaneous T-cell lymphoproliferations CD30+. It is characterized by an excellent prognosis and the treatment is therefore not very aggressive. However, its histological and molecular characteristics have many similarities with lymphoproliferative diseases whose prognosis is completely different. For this reason, it is important to study the patient from the anamnestic and clinical point of view in order to reach a correct diagnosis.