Non-compaction of the ventricular myocardium involving both ventricles is a rare condition and characterized by deeply increased trabeculations in one or more segments of the ventricle. Non-compaction is thought to be due to intrauterine arrest of compaction of the loosely interwoven meshwork present in fetal myocardial primordium. More recent studies suggest that non-compaction of the ventricular myocardium can be acquired later on in life sporadically.The apical segment of the left ventricle is most commonly affected, but biventricular involvement is also described. Herein, we describe an unusual case of biventricular non-compaction cardiomyopathy with left ventricular systolic and diastolic dysfunction. A 54-year-old man presented with clinical heart failure as well as arrhythmia. Transthoracic echocardiography revealed left ventricular non-compaction with depressed ejection fraction. Cardiac magnetic resonance imaging (MRI) further revealed right ventricular noncompaction.