Introduction- Various presentations of Mullerian ducts anomalies have been reported in the literature. This is a case report of Didelphys Uterus with a transverse vaginal septum and bilateral polycystic ovaries which was initially misdiagnosed as appendicitis and urolithiasis. Uterine didelphys constitutes 8.3% of all Mullerian duct anomalies. This index case was associated with polycystic ovaries which was not described in the classification of Mullerian ducts anomalies by the American Fertility Society. The delayed in diagnosis might have constituted distress and additional hospital cost to the patients. Case presentation- Here we present a 22 year patient with Didelphys uterus diagnosed at laparoscopy who presented with Primary Amenorrhea, cyclical abdominal pain, vagina septum and bilateral polycystic ovaries. Discussion/Conclusion- A combination of above symptoms is quite rare which may lead to delay in diagnosis and instituting therapy.

{"references": ["The American Fertility Society Classifications of adnexal adhesions, distal tubal obstruction, tubal occlusions secondary to tubal ligation, tubal pregnancies, Mullerian anomalies and intrauterine adhesions. FertilSteril. 1998; 49:944-55."]}