
Variation in the presentation of hereditary immunodeficiencies may be explained by genetic or environmental factors. Patients with mutations in HOIL1 (RBCK1) present with amylopectinosis-associated myopathy with or without hyper-inflammation and immunodeficiency. We report that barrier-raised HOIL-1-deficient mice exhibit amylopectin-like deposits in the myocardium but show minimal signs of hyper-inflammation. However, they show immunodeficiency upon acute infection with Listeria monocytogenes, Toxoplasma gondii or Citrobacter rodentium. Increased susceptibility to Listeria was due to HOIL-1 function in hematopoietic cells and macrophages in production of protective cytokines. In contrast, HOIL-1-deficient mice showed enhanced control of chronic Mycobacterium tuberculosis or murine γ-herpesvirus 68 (MHV68), and these infections conferred a hyper-inflammatory phenotype. Surprisingly, chronic infection with MHV68 complemented the immunodeficiency of HOIL-1, IL-6, Caspase-1 and Caspase-1;Caspase-11-deficient mice following Listeria infection. Thus chronic herpesvirus infection generates signs of auto-inflammation and complements genetic immunodeficiency in mutant mice, highlighting the importance of accounting for the virome in genotype-phenotype studies.
Rhadinovirus, immunology, Mice, Citrobacter, 2.1 Biological and endogenous factors, Innate, NF-kappaB, Listeriosis, Aetiology, Biology (General), Herpesviridae, murine gamma-herpesvirus 68, Q, Caspase 1, R, Herpesviridae Infections, Foodborne Illness, Infectious Diseases, Phenotype, Acute Disease, Medicine, Cytokines, Inflammation Mediators, Infection, Toxoplasma, QH301-705.5, Knockout, Ubiquitin-Protein Ligases, infectious disease, Science, Immunology, 610, Bone Marrow Cells, 616, Genetics, Animals, Humans, mouse, Listeria monocytogene, Inflammation, Interleukin-6, Prevention, Inflammatory and immune system, Macrophages, microbiology, Genetic Complementation Test, Immunity, Immunologic Deficiency Syndromes, Mycobacterium tuberculosis, Listeria monocytogenes, Immunity, Innate, Cell Compartmentation, Emerging Infectious Diseases, Good Health and Well Being, linear ubiquitination, Chronic Disease, Biochemistry and Cell Biology, immunodeficiency
Rhadinovirus, immunology, Mice, Citrobacter, 2.1 Biological and endogenous factors, Innate, NF-kappaB, Listeriosis, Aetiology, Biology (General), Herpesviridae, murine gamma-herpesvirus 68, Q, Caspase 1, R, Herpesviridae Infections, Foodborne Illness, Infectious Diseases, Phenotype, Acute Disease, Medicine, Cytokines, Inflammation Mediators, Infection, Toxoplasma, QH301-705.5, Knockout, Ubiquitin-Protein Ligases, infectious disease, Science, Immunology, 610, Bone Marrow Cells, 616, Genetics, Animals, Humans, mouse, Listeria monocytogene, Inflammation, Interleukin-6, Prevention, Inflammatory and immune system, Macrophages, microbiology, Genetic Complementation Test, Immunity, Immunologic Deficiency Syndromes, Mycobacterium tuberculosis, Listeria monocytogenes, Immunity, Innate, Cell Compartmentation, Emerging Infectious Diseases, Good Health and Well Being, linear ubiquitination, Chronic Disease, Biochemistry and Cell Biology, immunodeficiency
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