A nevus of the hair follicle of the hair scalp is described on a male child, aged three, white race, with curly hair "curly Hair nevus" and an epidermic nevus of the neck epidermis. The hair are thin, fair, disposed in curls with big spire in a number of two or three. They are short, without a 180 degrees torsion on their longitudinal axis. Transversally cut the section is almost circular. The nosology is discussed and the differential diagnosis is tried with the "woolly hair nevus".