Semicircular canal dehiscence (SCD) is a rare but clinically significant cause of vertigo and auditory symptoms. The clinical presentation is relatively specific and typically includes sound- or pressure-induced rotational vertigo accompanied by nystagmus, autophony, hypersensitivity to bone-conducted sound (hyperacusis), and pseudo-conductive hearing loss. Imaging plays a central role in establishing an accurate diagnosis and in excluding differential diagnoses. High-resolution thin-slice computed tomography (CT), particularly when combined with magnetic resonance imaging (MRI), forms the cornerstone of radiologic assessment. Importantly, a substantial proportion of patients with radiologically confirmed dehiscence remain asymptomatic. While the presence of vestibular symptoms in conjunction with a bony dehiscence should raise suspicion for SCD syndrome, other etiologies must be prioritized in the differential diagnosis based on clinical history, examination, and imaging findings, given the rarity of the condition.