Infection with Dracunculus medinensis of the vulva is rare. It was clinically misdiagnosed as a neoplastic growth. It was characterised by an oval, firm, mobile swelling in the middle of the left labia majora. The cut surface showed white-coloured, thread-like, coiled- up adult parasite embedded in the central portion of the growth. Histopathology showed transverse and obliquely cut sections of the adult parasite surrounded by a danse fibrocollagenous stroma, infiltrated by lymphocytes, plasma cells and a few eosinophils.