The authors report two recent cases of Fenton's syndrome, a very rare carpal fracture-dislocation. After some anatomico-physiopathological considerations and a review of the literature, a wider nosographic frame is proposed in which the entity of the dislocation of the head of the capitate bone is not essential. According to both the literature and the personal findings, the authors remark that this syndrome is always found in the presence of two morphological variants of the distal radioulnar joint. Finally, the authors stress the importance of a correct diagnosis of this lesion to avoid unnecessary attempts of reduction.