Cerebral venous thrombosis is a rare and life threatening condition that should be considered in all individual with unusual and intractable headache. Young adults and children are typically affected and the superior sagittal sinus is most often concerned by thrombosis. MRI is the most sensitive examination technique and is now required for early diagnosis, leading to an improved prognosis. One or several prothrombotic risk factors are identified in most patients but about 20% of cerebral venous thrombosis have no cause identified. Anticoagulation is started as soon as the diagnosis is considered, even in the presence of hemorrhagic infarcts, and rapidly improves the condition in most patients. In situ thrombolysis is exceptionally delivered.