ABSTRACTIn 2005, the World Health Organization renamed the lesion, previously known as an odontogenic keratocyst, as the keratocystic odontogenic tumor (KOT or KCOT). The term odontogenic keratocyst (OKC) was first used by Philipson in 1963 and its clinical and histologic features were confirmed by Browne in 1970 and 1971. In this case report, a young patient with a histology report as an orthokeratinized variety of KCOT and it was a primary lesion with amcystic lining that was thick may be due to chronic irritation because of which it could be removed in toto. Resection was not advocated as it causes morbidity, peripheral ostectomy could not be performed as the buccal and lingual cortical plates were already thinned out with areas of perforation. Thus, enucleation with Carnoy's solution was considered ideal for this case. Also, this patient has been on regular follow-up for around 8 months showed good healing with no signs of recurrence.How to cite this articleRamaswami R, Galinde J, Srivalli N, Sidana S. Keratocystic Odontogenic Tumor. J Contemp Dent 2013;3(2):87-91.