Background. Growing skull fracture or craniocerebral erosion is a rare complication of linear skull fracture in childhood. It is characterized by progressive diastatic enlargement of the fracture line, which leads to a cranial defect, dural cleft, and cerebral herniation. It is presented as a soft pulsabile scalp swelling above the fracture, with a clear cranial defect. Case report. In this paper we presented a patient, an 8-month-old boy with the growing skull fracture revealed four weeks after the injury. After the surgical treatment, the boy was in a good general condition without the presence of neurologic impairment. Conclusion. Early recognition of craniocerebral erosion is very important. Timely detection prevents further progression of the disease and the evolution of neurological impairment. Surgery is the method of choice for treating a growing skull fracture .