A review is made of 234 cases of choroid plexus papillomas collected from the literature, to which 11 unpublished personal cases are added.The clinical features, plain roentgenographic findings of the skull, and the value of pneumography, cerebral angiography and gamma encephalography in establishing the diagnosis are discussed in detail.The majority of choroid plexus papillomas occurred within the first decade of life and were invariably associated with hydrocephalus.Suture separation, craniofacial disproportion, increased digital markings and other roentgenographic changes of increased intracranial pressure provide no specific proof as to the nature of location or the underlying pathology.