Saif Ghabisha,1 Faisal Ahmed,2 Saleh Al-wageeh,1 Ebrahim Al-shami,2 Khalil Al-naggar,2 Ghamdan Obaid,3 Mohammad Reza Askarpour4 1Department of General Surgery, Ibb University of Medical Science, Ibb, Yemen; 2Urology Research Center, Al-Thora General Hospital, Department of Urology, Ibb University of Medical Science, Ibb, Yemen; 3Department of Orthopedy, Ibb University of Medical Science, Ibb, Yemen; 4Department of Urology, Shiraz University of Medical Sciences, Shiraz, IranCorrespondence: Faisal AhmedUrology Research Center, Al-Thora General Hospital, Department of Urology, Ibb University of Medical Science, Alodine Street, Ibb, YemenTel +967 776089579Email fmaaa2006@yahoo.comAbstract: Cord congenital hernia is a condition in which due to a patent umbilical ring, intestinal components protrude into the umbilical cord. Although post-natal umbilical hernia is not uncommon, its congenital form is an uncommon phenomenon (incidence rate about 0.2%) with an excellent post-surgical prognosis. It is frequently misdiagnosed as a small omphalocele. Additionally, if it is undiagnosed at the time of birth, clamping the umbilical cord can cause iatrogenic atresia of the ileum. Hence, during a physical exam, it is mandatory to look carefully for any skin folds in the form of a collar or defects in the umbilical ring or abdominal wall to avoid misdiagnosis. We report a full-term male newborn present with umbilical cord hernia, who underwent successful open surgery, with extra focus on the management and outcome of this disease.Keywords: abdominal wall, congenital abnormalities, omphalocele, umbilical cord hernia