<p>The presence of a nasal vestibule mass can be challenging in obtaining diagnosis and treatment due to the features of nasal vestibule. There are various types of diseases that can involve the nasal vestibule. Here, we presented the case of a patient with swelling of the right nasal vestibule and was incidentally diagnosed histopathologically as trichofolliculoma, a rare skin lesion. We discussed the characteristics of trichofolliculoma disease and presented a diagnosis, necessary treatment of this case and related literature review.</p>