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Case for diagnosis

descriptionPublicationkeyboard_double_arrow_right Article , Other literature type 01 Jun 2014Publisher:FapUNIFESP (SciELO)Journal:Anais Brasileiros de Dermatologia, volume 89, pages 521-522 (eissn: 0365-0596,

Authors: Lima, Lourenço de Azevedo; Haddad, Natacha de Carvalho Mello; Lima, Ricardo Barbosa; D'Acri, Antonio Macedo; Martins, Carlos José;

doi: 10.1590/abd1806-4841.20142863

pmid: 24937836

pmc: PMC4056720

Case for diagnosis

- Summary
- Subjects
- Metrics

Abstract

Degos disease, also known as malignant atrophic papulosis, is a rare occlusive vasculopathy of unknown etiology characterized by infarcts in the dermis, gastrointestinal tract, central nervous system, and other organs. It is characterized by papules, which become umbilicated and evolve with a depressed porcelain-white central area, with an erythematous halo with telangiectasias. Histological findings include wedge-shaped dermoepidermal necrosis and blood vessel thrombosis. Approximately 50-60% of patients with systemic symptoms die within 2-3 years, most due to gastrointestinal perforation. We report a typical case, with lethal outcome, in a 45-year-old woman.

Related Organizations

Federal University of Rio de Janeiro
Brazil

Keywords

Venous Thrombosis, Biopsy, Complement C5, Dermatology, Middle Aged, Malignant Atrophic Papulosis, Fatal Outcome, Intestinal Perforation, RL1-803, Humans, Female, Malignant atrophic papulosis, What Is Your Diagnosis?, Vascular diseases, Skin

Impact byBIP!

	citations This is an alternative to the "Influence" indicator, which also reflects the overall/total impact of an article in the research community at large, based on the underlying citation network (diachronically).	5
	popularity This indicator reflects the "current" impact/attention (the "hype") of an article in the research community at large, based on the underlying citation network.	Average
	influence This indicator reflects the overall/total impact of an article in the research community at large, based on the underlying citation network (diachronically).	Top 10%
	impulse This indicator reflects the initial momentum of an article directly after its publication, based on the underlying citation network.	Average