A rare case of aplasia of the mandibular condyle is presented along with the tomographic findings. A 31-year-old Caucasian woman presented with a main complaint of facial asymmetry. No family history or any trauma was found. A CT study was performed and the sagittal CT view demonstrated a complete absence of the left condyle. This case of unknown aetiology was thoroughly examined and, based on clinical findings, we suggest that it could be of developmental origin.