AbstractA pregnant woman at 32 weeks of gestation was referred because of untypical visualization of a three‐vessel tracheal view. Detailed ultrasound examination demonstrated an abnormal position of descending aorta, positioned at the right‐front side of the spine at the level of four‐chamber view. The descending aorta was connected with left pulmonary artery through ductus arteriosus, which configured a vascular ring. Right aortic arch with mirror‐image branching without any associated anomaly was suspected prenatally. Amniocentesis showed no chromosomal abnormality. A male, 2440‐g infant was delivered vaginally at 37 weeks and 4 days of gestation. Echocardiography confirmed no associated congenital heart defect. Three‐dimensional reconstruction using 64‐slice spiral computed tomography angiography at 2‐months old confirmed the diagnosis of right aortic arch with mirror‐image branching. The infant is now 1 year old and well developed without any symptoms.