Peripheral retinal neovascularization occurs in many diseases, including sickle-cell disease, Eales disease, and sarcoidosis. To our knowledge, combined retinal detachment with peripheral retinal neovascularization has not been reported in the literature.We examined a 14-year-old girl with Turner syndrome. Total rhegmatogenous retinal detachment and tractional retinal detachment were found in the left eye, and peripheral avascular zone with neovascularization was found in both eyes. The retinal detachment was treated with an encircling scleral buckle. Subsequent retinal photocoagulation over the avascular zones of both eyes was performed.Retinal neovascularizations regressed, and the retinal detachment reattached after treatment.Retinal neovascularization, rhegmatogenous retinal detachment, and tractional retinal detachment can be ocular findings associated with Turner syndrome. Retinal photocoagulation over the avascular zone is a possible treatment for neovascularization.