Dyschromatosis universalis hereditaria is a rare inherited pigmentary disorder. It has a characteristic reticulate pigmentation involving the entire body, with acral sparing. The case is reported here for its unusual involvement of acral areas and reduced dermatoglyphs. Furthermore, dermoscopic patterns of this disease are reported very rarely in the literature. We observed various patterns in dermoscopy, namely monotonous, reticulate and diffuse with a ‘starry sky’ appearance.