Abstract Basidiobolomycosis is a rare fungal disease caused by Basidiobolus ranarum , which is an environmental saprophyte. It is a chronic inflammatory disease that is generally restricted to the subcutaneous tissue and rarely involves the gastrointestinal tract. With the intent to spread awareness of this potentially life threatening and rare infection, we report a 4-year-old boy presenting with abdominal pain and fever with eventual diagnosis of gastrointestinal basidiobolomycosis. We discuss the nonspecific and confusing symptoms of this rare infection and available treatment options in detail.