A girl, having an echocardiogram suggestive of double aortic arch, underwent a cardiac multidetector computed tomography (MDCT) examination. MDCT revealed double aortic arch with left arch atresia distal to the left subclavian artery. The left common carotid artery and the left subclavian artery arose from the left arch, the right common carotid artery and the right subclavian artery originated from the right arch (Fig. 1). Moderate compression of the trachea within the vascular ring was also noted (Fig. 2). Surgical intervention was not performed because of the absence of symptoms due to compression of the oesophagus or trachea.