Myxoma is a rare bone tumor of the jaws. The exact aetiology and pathogenesis of this tumor still remains obscure. The tumor is frequently seen in young adults and in the mandible. Enucleation or local curetting have been recommended in the literature as the treatments of choice, although some authors have suggested more radical procedures because of the recurrences. In this paper a case of myxoma of the mandible and a review of the literature is presented.