Fibrosclerotic and fibroinflammatory diseases are pelicular and unusual conditions, which may present in any part of the body. Howeverm, in the region of the head and the neck they are seldom seen and hence easily misdiagnosed. To date, about twenty-two such cases have been reported in the head and neck region. Presented here is a case of tumefactive fibroinflammatory disease of the neck in an 85-year-old woman with a detailed account of the clinical features, cytology, histology and postmortem findings. Also presented is a brief overview of the literature pertaining of this condition.