The anaesthetic management of a patient with Emery-Dreifuss muscular dystrophy

descriptionPublicationkeyboard_double_arrow_right Article 01 Sep 1996 English Publisher:Springer Science and Business Media LLCJournal:Canadian Journal of Anaesthesia, volume 43, pages 968-971 (issn: 0832-610X, eissn: 1496-8975,

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Authors: V, Jensen;

doi: 10.1007/bf03011813

pmid: 8874917

The anaesthetic management of a patient with Emery-Dreifuss muscular dystrophy

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Abstract

This case report presents a patient with Emery-Dreifuss Muscular Dystrophy and describes the anaesthetic considerations.The features of Emery-Dreifuss Muscular Dystrophy are contractures, humeroperoneal muscle weakness and cardiomyopathy. The anaesthetic considerations for this syndrome are difficult tracheal intubation, difficult spinal anaesthetic, heart block, gastric reflux, rhabdomyolysis, and unproved malignant hyperthermia susceptibility.The major anaesthetic problem for the patient with Emery-Dreifuss Muscular Dystrophy could be a life-threatening cardiomyopathy.

Related Organizations

University of Alberta
Canada

Keywords

Adult, Male, Humans, Anesthesia, Muscular Dystrophies

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