A rare case of Embryonal Rhabdomyosarcoma in a 5 year male child involving Nasopharynx with intracranial. secondaries is reported. The child presented with difficulty in breathing and swallowing with change of the voice and bleeding from nose and mouth off and on. Histopathology of the excised mass proved the diagnosis of RMS & CT scan showed secondaries in the left frontal & temporal to be of brain. In spite of the surgery and chemotherapy, the disease proved to be fatal within 3 months of diagnosis.