Cleidocranial dysplasia (CCD) is a generalised disorder of bone ossification, the most obvious sites of involvement being the skull and the clavicles. Two patients ,are described in whom a variety of disorders were considered before the diagnosis was made on the basis of the radiological features. It is pos sible that this is an underdiagnosed entity, because of its relatively benign clinical effects. It should be considered in the differential diagnosis of short stature with features of skeletal immaturity like abnormally large skull fontanella and Wonnian bones.