This article reviews a case of small-bowel polyposis associated with a primary jejunal adenocarcinoma in a patient who had previously undergone a subtotal colectomy for familial colonic polyposis. The patient was seen for a spontaneously resolving, subacute small-bowel obstruction secondary to metastatic mesenteric and serosal nodules. The jejunal malignancy was metastatic to the lungs in the form of lymphangitic spread, the patient subsequently dying after an open-lung biopsy in an attempt to establish a diagnosis. This particular combination of clinical features, especially the pulmonary findings, appears not to have been previously reported.