A case of fibromyxoma of the long bone is presented. This benign bone tumor is more often found in the bones of the jaw, but is a rare lesion in extragnathic bones. IN the presented case of a 28-year-old man the tumor was situated in the right femoral neck. In the roentgenograms it showed a cast-like osteolytic defect with unclear marginal sclerosis and patchy densities within the lesion. Histologically, the tumor consisted of a proliferating hypocellular myxomatous tissue with some focal calcification and fibrous areas. No chondroid pattern was present and there was no clear lobulation. Differential diagnostic considerations include ganglia of bone, chondromyxoid fibroma, chondrosarcoma and fibrosarcoma, all of which may contain prominently myxoid zones.