AbstractExtranodal marginal zone B‐cell lymphomas (EMZLs), while relatively common in adults, are rare entities in the pediatric population. A subclass of the typically aggressive non‐Hodgkin lymphomas, the few reported pediatric cases indicate that, as in adults, these tumors tend to be indolent. We present a case of EMZL arising in the conjunctivae in a 9‐year‐old male with bilateral disease. The patient was treated with surgical excision alone and has remained disease‐free 6 years after the operation. Pediatr Blood Cancer. 2010;55:1414–1416. © 2010 Wiley‐Liss, Inc.