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Familial Progressive Sensorineural Deafness

Authors: Shigeru Sugiura; Michael M. Paparella; Tomoyuki Hoshino;

Familial Progressive Sensorineural Deafness

Abstract

DEAFNESS resulting from genetic causes may be present at time of birth (congenital) or may develop subsequent to birth (acquired). In congenital deafness the end-or-gan of hearing may not develop in the first trimester (aplasia). It is also conceivable, but not proven, that a fully differentiated sense organ may degenerate during the second and third trimester of pregnancy. The aplasias are generally accepted as being congenital and nonprogressive. Genetic deafness may first become apparent during infancy, childhood, or early adult life and thedeafnessmay be considered acquired although the genetic deficiency is obviously not.1 Goodhill2has divided hereditary deafness occurring after birth into infantile and adult types. According to the age of onset of genetic deafness (heredodegenerative) Cawthorne3believed there is a continuous distribution, beginning either in early infancy or throughout childhood, up to the age of 30 years. Heredodegenerative deafness is usually progressive and

Keywords

Male, Audiometry, Ear, Inner, Ear, Middle, Humans, Temporal Bone, Female, Deafness, Middle Aged, Aged, Cochlea

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    26
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    influence
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Found an issue? Give us feedback
citations
This is an alternative to the "Influence" indicator, which also reflects the overall/total impact of an article in the research community at large, based on the underlying citation network (diachronically).
BIP!Citations provided by BIP!
popularity
This indicator reflects the "current" impact/attention (the "hype") of an article in the research community at large, based on the underlying citation network.
BIP!Popularity provided by BIP!
influence
This indicator reflects the overall/total impact of an article in the research community at large, based on the underlying citation network (diachronically).
BIP!Influence provided by BIP!
impulse
This indicator reflects the initial momentum of an article directly after its publication, based on the underlying citation network.
BIP!Impulse provided by BIP!
26
Average
Top 10%
Top 10%
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