descriptionPublicationkeyboard_double_arrow_right Article 01 Jun 1983 English Publisher:American Medical Association (AMA)Journal:Archives of Internal Medicine, volume 143, page 1,266 (issn: 0003-9926,

Authors: C. Richard Dickersin; Howard J. Fingert; Ira T. Lott; Oliver W. Press;

doi: 10.1001/archinte.1983.00350060198036

pmid: 6860058

Pancytopenia in Mannosidosis

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Abstract

A case of autoimmune pancytopenia is described in a patient with mannosidosis who developed anti-platelet and anti-neutrophil antibodies and a low haptoglobin level. Bone marrow biopsy and 111InCl3 bone marrow scanning demonstrated hypoplasia of the marrow with a paucity of "storage cells." Pathogenic mechanisms and implications for other inborn errors of metabolism are discussed.

Related Organizations

Harvard University
United States
University of Mary
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University of Washington
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Keywords

Adult, Blood Platelets, Male, Haptoglobins, Neutrophils, Pancytopenia, Bone Marrow Examination, Mannosidases, Humans, Mannose, Carbohydrate Metabolism, Inborn Errors

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