publication . Other literature type . Article . 1985

Abnormalities of the lungs and thoracic cage in the Ehlers-Danlos syndrome.

J. G. Ayres; F. M. Pope; J. F. Reidy; T. J. H. Clark;
Open Access
  • Published: 01 Apr 1985
  • Publisher: BMJ
Twenty patients with the Ehlers-Danlos syndrome, (10 type I, six type II, and four type IV) were studied to assess the frequency of respiratory abnormalities in this condition. Five patients (25%) had had at least one episode of haemoptysis, but none had any defect of coagulation. There was a high frequency of recurrent sinusitis, notably in those with the type I syndrome. Two patients had bullous lung disease, one of whom (type IV) had had three pneumothoraces and subsequent pleurodesis; he also had tracheomegaly (the Mounier-Kuhn abnormality). Minor skeletal abnormalities such as pectus excavatum were common, particularly in patients with type IV disease. Thre...
free text keywords: Research Article, Pulmonary and Respiratory Medicine, Respiratory system, Pleurodesis, medicine.medical_treatment, medicine, Pneumothorax, medicine.disease, Gastroenterology, medicine.medical_specialty, Lung, medicine.anatomical_structure, Surgery, Lung volumes, Ehlers–Danlos syndrome, business.industry, business, Internal medicine, Pectus excavatum, Respiratory disease
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Other literature type . 1985
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Other literature type . 1985
Provider: Datacite
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