
Objetivos: La linfangiectasia intestinal primaria es un trastorno del sistema linfático, en el que debido a obstrucción del drenaje linfático se produce malabsorción, enteropatía pierde-proteínas e hipogammaglobulinemia, y consecuentemente una malnutrición en diverso grado. Su tratamiento es complejo e incluye medidas dietéticas y farmacológicas. Material y método: En este artículo se expone el caso de una mujer de 35 años con ascitis quilosa de repetición, precisando varios ingresos hospitalarios y paracentesis evacuadoras. Tras ser diagnosticada de linfangiectasia intestinal primaria, la instauración de dietoterapia sustituyendo las grasas alimentarias por aceite MCT, ha permitido una evolución favorable tanto desde el punto de vista clínico como analítico y antropométrico. Conclusiones: El empleo de una dieta específica y el uso de triglicéridos de cadena media en la linfangiectasia intestinal son el pilar principal del tratamiento en este caso, mejorando su sintomatología y estado nutricional. Precisa de alto nivel de adherencia y colaboración por parte del paciente, siendo necesario el control médico periódico de por vida, dado que la evolución a largo plazo no es bien conocida.
MCT, Linfangiectasia, Lymphangiectasia, Medical Subject Headings::Diseases::Hemic and Lymphatic Diseases::Lymphatic Diseases::Lymphangiectasis::Lymphangiectasis, Intestinal, Medical Subject Headings::Diseases::Pathological Conditions, Signs and Symptoms::Pathologic Processes::Disease Attributes::Recurrence, Medical Subject Headings::Named Groups::Persons::Age Groups::Adult, Chylosa ascites, Ascitis quilosa, Medical Subject Headings::Diseases::Digestive System Diseases::Peritoneal Diseases::Chylous Ascites, Dietoterapia, Diet-therapy, Medical Subject Headings::Check Tags::Female, Medical Subject Headings::Organisms::Eukaryota::Animals::Chordata::Vertebrates::Mammals::Primates::Haplorhini::Catarrhini::Hominidae::Humans
MCT, Linfangiectasia, Lymphangiectasia, Medical Subject Headings::Diseases::Hemic and Lymphatic Diseases::Lymphatic Diseases::Lymphangiectasis::Lymphangiectasis, Intestinal, Medical Subject Headings::Diseases::Pathological Conditions, Signs and Symptoms::Pathologic Processes::Disease Attributes::Recurrence, Medical Subject Headings::Named Groups::Persons::Age Groups::Adult, Chylosa ascites, Ascitis quilosa, Medical Subject Headings::Diseases::Digestive System Diseases::Peritoneal Diseases::Chylous Ascites, Dietoterapia, Diet-therapy, Medical Subject Headings::Check Tags::Female, Medical Subject Headings::Organisms::Eukaryota::Animals::Chordata::Vertebrates::Mammals::Primates::Haplorhini::Catarrhini::Hominidae::Humans
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