Though developmental defects of human dentition are not uncommon, agenesis of teeth in a patient who also presents with a supernumerary tooth, is one of the rare numerical anomalies in human dentition known as concomitant hypo-hyperdontia. Due to its occasional occurrence and lack of knowledge about hypo-hyperdontia, diagnosing this condition may be difficult or may be missed by dental practitioners. Many syndromes may also mask early detection of these cases, thus neglecting many treatment planning considerations of the dentition. This review paper presents literature on concomitant hypo­ hyperdontia at a glance, so that clinicians can derive assistance in dealing with this anomaly, should they ever come across it.