publication . Article . 2020

Febrile infection-related epilepsy syndrome: long-term consequences (own observations)

Open Access
  • Published: 01 May 2020 Journal: Russian Journal of Child Neurology, volume 15, pages 40-46 (issn: 2073-8803, eissn: 2412-9178, Copyright policy)
  • Publisher: Publishing House ABV Press
Abstract
<jats:p>Febrile infection-related epilepsy syndrome (FIRES) is an exceedingly rare disorder that affects 1 in 1.000.000 children. However, we believe that FIRES is more common, since many cases remain undiagnosed. The exact pathogenesis of this clinical syndrome is still poorly understood. There are several theories of its development, including immune, genetic, and inflammatory-mediated ones. FIRES is known to have dismal outcomes with a death rate of up to 30 % in the acute phase and subsequent development (often immediately after the acute phase) of refractory epilepsy and mental retardation in 66–100 % of survivors. Despite the increasing number of publicati...
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free text keywords: febrile seizures, febrile infection-related epilepsy syndrome, encephalitis, neuropsychological diagnosis, focal epilepsy, drug resistance, Carbamazepine, medicine.drug, medicine, Epilepsy syndromes, Febrile infection related epilepsy syndrome, Mortality rate, Cognition, business.industry, business, Pediatrics, medicine.medical_specialty, Epilepsy, medicine.disease, Oxcarbazepine, Status epilepticus, medicine.symptom, lcsh:Neurology. Diseases of the nervous system, lcsh:RC346-429
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