publication . Report . Article . 2017

Fibroelastose pleuroparenquimatosa: relato de dois casos no Brasil

Paula S. Gomes; Christina Shiang; Gilberto Szarf; Ester Nei Aparecida Martins Coletta; Carlos Alberto de Castro Pereira;
Open Access English
  • Published: 01 Feb 2017
  • Publisher: Sociedade Brasileira de Pneumologia e Tisiologia
ABSTRACT Pleuroparenchymal fibroelastosis (PPFE) is a rare lung disease. It can be idiopathic or associated with any one of various conditions. To our knowledge, this is the first report of two cases of PPFE in Brazil. Our first patient presented with pleural and subpleural fibrosis in the upper lobes; a spiculated nodule in the left upper lobe; and a mild reticular pattern in the lower lobes. Surgical lung biopsy revealed PPFE in the upper lobes, including the nodule, and unclassified interstitial pneumonia in the left lower lobe. Our second patient had a history of exposure to domestic birds, indicating a risk of hypersensitivity pneumonitis, and presented wit...
free text keywords: Lung diseases, interstitial/diagnosis, Lung diseases, interstitial/etiology, Alveolitis, extrinsic allergic, Case Report, Doenças pulmonares intersticiais/diagnóstico, Doenças pulmonares intersticiais/etiologia, Alveolite alérgica extrínseca, Left lower lobe, Lung transplantation, medicine.medical_treatment, medicine, Pathology, medicine.medical_specialty, Lung disease, Hypersensitivity pneumonitis, medicine.disease, business.industry, business, Lung biopsy, Interstitial pneumonia, Reticular Pattern, Lung, medicine.anatomical_structure, lcsh:Diseases of the respiratory system, lcsh:RC705-779
Related Organizations
18 references, page 1 of 2

Travis, WD, Costabel, U, Hansell, DM, King, TE, Lynch, DA, Nicholson, AG. An official American Thoracic Society/European Respiratory Society statement Update of the international multidisciplinary classification of the idiopathic interstitial pneumonias. Am J Respir Crit Care Med. 2013; 188 (6): 733-748 [OpenAIRE] [PubMed]

Portillo, K, Guasch Arriaga, I, Ruiz-Manzano, J. Pleuroparenchymal fibroelastosis is it also an idiopathic entity?. Arch Bronconeumol. 2015; 51 (10): 509-514 [PubMed]

Davies, D, Crowther, JS, MacFarlane, A. Idiopathic progressive pulmonary fibrosis. Thorax. 1975; 30 (3): 316-325 [OpenAIRE] [PubMed]

Amitani, R, Niimi, A, Kuze, F. Idiopathic pulmonary upper lobe fibrosis. Kokyu. 1992; 11: 693-699

Kawabata, Y, Matsuoka, R. Pathology of idiopathic pulmonary upper lobe fibrosis. Nihon Kyobu Rinsho. 2003; 62: S161-S202

Frankel, SK, Cool, CD, Lynch, DA, Brown, KK. Idiopathic pleuroparenchymal fibroelastosis Description of a novel clinicopathologic entity. Chest. 2004; 126 (6): 2007-2013 [PubMed]

Watanabe, K. Pleuroparenchymal fibroelastosis its clinical characteristics. Curr Respir Med Rev. 2013; 9: 299-237 [OpenAIRE] [PubMed]

Oda, T, Ogura, T, Kitamura, H, Hagiwara, E, Baba, T, Enomoto, Y. Distinct characteristics of pleuroparenchymal fibroelastosis with usual interstitial pneumonia compared with idiopathic pulmonary fibrosis. Chest. 2014; 146 (5): 1248-1255 [PubMed]

Cuppens, K, Verbeken, E, Coolen, J, Verschakelen, J, Wuyts, W. Idiopathic pleuroparenchymatous fibroelastosis A case report and brief review of the literature. Respir Med Case Rep. 2014; 12: 7-9 [OpenAIRE] [PubMed]

von der Thüsen, JH, Hansell, DM, Tominaga, M, Veys, PA, Ashworth, MT, Owens, CM. Pleuroparenchymal fibroelastosis in patients with pulmonary disease secondary to bone marrow transplantation. Mod Pathol. 2011; 24 (12): 1633-1639 [OpenAIRE] [PubMed]

Beynat-Mouterde, C, Beltramo, G, Lezmi, G, Pernet, D, Camus, C, Fanton, A. Pleuroparenchymal fibroelastosis as a late complication of chemotherapy agents. Eur Respir J. 2014; 44 (2): 523-527 [PubMed]

Nakatani, T, Arai, T, Kitaichi, M, Akira, M, Tachibana, K, Sugimoto, C. Pleuroparenchymal fibroelastosis from a consecutive database a rare disease entity?. Eur Respir J. 2015; 45 (4): 1183-1186 [PubMed]

Camus, P, von der Thüsen, J, Hansell, DM, Colby, TV. Pleuroparenchymal fibroelastosis one more walk on the wild side of drugs?. Eur Respir J. 2014; 44 (2): 289-296 [PubMed]

Machuca, JS, Niazi, M, Diaz-Fuentes, G. Pleuroparenchymal fibroelastosis presenting as a hypermetabolic lung nodule. J Bronchology Interv Pulmonol. 2011; 18 (1): 65-68 [PubMed]

Baroke, E, Heussel, CP, Warth, A, Eichinger, M, Oltmanns, U, Palmowski, K. Pleuroparenchymal fibroelastosis in association with carcinomas. Respirology. 2016; 21 (1): 191-194 [PubMed]

18 references, page 1 of 2
Any information missing or wrong?Report an Issue