Biliary atresia is a severe and progressive inflammatory process of unknown cause, which initially involves the extrahepatic bile ducts but which quickly proceeds towards the intrahepatic bile tree leading rapidly to biliary cirrhosis. Biliary atresia is the major reason for liver transplantation during childhood. The extrahepatic bile ducts in biliary atresia become connective fibrotic cords which is irreversibly damaged.
mesheuropmc: congenital, hereditary, and neonatal diseases and abnormalitiesotorhinolaryngologic diseases
free text keywords: MED/38 Pediatria generale e specialistica, MED/20 Chirurgia pediatrica e infantile