publication . Article . 2013

Combined Bentall and modified Ravitch procedures in a patient with Marfan syndrome

Bhuvnesh Kansara; Ajmer Singh; Samir Girotra; K S Iyer;
Open Access English
  • Published: 01 Jan 2013 Journal: Journal of Anaesthesiology, Clinical Pharmacology, volume 29, issue 1, pages 95-98 (issn: 0970-9185, eissn: 2231-2730, Copyright policy)
  • Publisher: Medknow Publications & Media Pvt Ltd
Abstract
Marfan syndrome is an inherited, connective-tissue disorder transmitted as an autosomal dominant trait. Cardinal features of the disorder include tall stature, ectopia lentis, mitral valve prolapse, aortic root dilatation, and aortic dissection. Pectus excavatum may exist as an isolated lesion or in association with a genetic syndrome such as Marfan syndrome. We report the successful management of a simultaneous correction of pectus excavatum and the underlying cardiovascular diseases.
Subjects
mesheuropmc: musculoskeletal diseases
free text keywords: Aortic aneurysm, Marfan syndrome, Anesthesiology, Case Report, pectus excavatum, RD78.3-87.3, Pharmacy and materia medica, RS1-441

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publication . Article . 2013

Combined Bentall and modified Ravitch procedures in a patient with Marfan syndrome

Bhuvnesh Kansara; Ajmer Singh; Samir Girotra; K S Iyer;