Original Solution for Middle Ear Implant and Anesthetic/Surgical Management in a Child with Severe Craniofacial Dysmorphism

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Giovanni Bianchin ; Lorenzo Tribi ; Aronne Reverzani ; Patrizia Formigoni ; Valeria Polizzi (2015)
  • Publisher: Hindawi Limited
  • Journal: Case Reports in Otolaryngology, volume 2,015 (issn: 2090-6765, eissn: 2090-6773)
  • Related identifiers: doi: 10.1155/2015/205972, pmc: PMC4602318
  • Subject: RF1-547 | Case Report | Article Subject | Otorhinolaryngology
    mesheuropmc: otorhinolaryngologic diseases

We describe the novel solution adopted in positioning middle ear implant in a child with bilateral congenital aural atresia and craniofacial dysmorphism that have posed a significant challenge for the safe and correct management of deafness. A five-year-old child, affected by a rare congenital disease (Van Maldergem Syndrome), suffered from conductive hearing loss. Conventional skin-drive bone-conduction device, attached with a steel spring headband, has been applied but auditory restoration was not optimal. The decision made was to position Vibrant Soundbridge, a middle ear implant, with an original surgical application due to hypoplasia of the tympanic cavity. Intubation procedure was complicated due to child craniofacial deformities. Postoperative hearing rehabilitation involved a multidisciplinary team, showing improved social skills and language development.
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