Profuse coarse pulmonary nodules in a patient with lymphangioleiomyomatosis: thirty-three years of follow-up

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Rasmussen, Daniel B. ; Shaker, Saher B. ; Seersholm, Niels ; Colella, Sara ; Clementsen, Paul F. (2014)

Lymphangioleiomyomatosis (LAM) is a rare disease characterized by progressive cystic destruction of the lungs. We present an unusual radiological presentation of lymphangioleiomyomatosis in a patient followed for 33 years with profuse coarse lung nodules in addition to the classical cystic lesions. We believe that this report might support the case for considering LAM a low-malignant neoplasm.Keywords: Lymphangioleiomyomatosis; cysts; nodules; neoplasm(Publishedf: 9 December 2014)Citation: European Clinical Respiratory Journal 2014, 1: 26272 - http://dx.doi.org/10.3402/ecrj.v1.26272
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